(C4) Butyrylcarnitine
| Artikel-Nr. | Packungseinheit | Preis | Vorlaufzeit | Jetzt kaufen |
|---|---|---|---|---|
| 4266-1mg | 1 mg | auf Anfrage | 7 Tagen. |
Butyrylcarnitine, also known as (3R)-3-(butyryloxy)-4-(trimethylammonio)butanoate or L-carnitine butyryl ester, is classified as a member of the acylcarnitines. Acylcarnitines are organic compounds containing a fatty acid with the carboxylic acid attached to carnitine through an ester bond. Butyrylcarnitine may be used as an analytical reference standard for the separation and identification of underivatized butyryl-L-carnitine in human plasma samples using high-performance liquid chromatography coupled to tandem mass spectrometry (HPLC-MS/MS).
Butyrylcarnitine can be used to study its role in energy production and its metabolic effects, to understand metabolic diseases and conditions associated with mitochondrial dysfunction. Butyrylcarnitine is a major biological marker of short-chain acyl-CoA dehydrogenase deficiency, glutaric acidemia type II and isobutyrylglycinuria, and ethylmalonic encephalopathy.
The product is used primarily as a control for MS/MS.
General properties
| Appearance: | white solid |
| Molecular weight: | 267.75 |
| CAS number: | 162067-50-7 (chloride), 25576-40-3 (inner salt) |
| Molecular formula: | C11H22ClNO4 |
| Solubility: | DMSO, DMF, ethanol |
| Quality control: | NMR 1H and HPLC-MS (95+%) |
| Storage conditions: | 24 months after receival at -20°C in the dark. Transportation: at room temperature for up to 3 weeks. Desiccate. |
| Sicherheitsdatenblatt: | herunterladen |
| Product specifications |
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